Jin-Seok Kim, MD Department of Cardiology, Sejong Heart Institute, Sejong General Hospital. Bucheon, Gyeonggi-do, Korea Arrhythmogenic right ventricular dysplasia/cardiomyopathy ABSTRACT Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a clinical entity characterized by ventricular arrhythmias and a specific ventricular pathology showing fibrofatty infiltration of the right ventricular (RV) free wall. ARVD/C is known as an important cause of sudden cardiac death in young adults. We reported a case of a 38-year-old female who visited us for palpitation and a history of syncope, and was diagnosed with ARVD/C. Ventricular arrhythmias such as frequent ventricular premature beats and ventricular tachycardia were documented. Also, RV enlargement and dysfunction were noted on imaging. Finally, she received an ICD implantation. Key words: ventricular tachycardia arrhythmogenic right ventricular dysplasia cardiomyopathy Received: June 28, 2010 Revision Received: August 11, 2010 Accepted: Correspondence: Jin-Seok Kim, MD, Division of Cardiology, Department of Cardiology, Sejong Heart Institute, Sejong General Hospital. 91-121 Sosabon-2-dong, Sosa-gu, Bucheon 422-711, Korea Tel: 82-32-340-1155, Fax: 82-32-349-3005 E-mail: heartmania@nate.com 39
A B Figure 1. Baseline ECG on admission (A) and follow-up (B). A. Frequent ventricular ectopies with LBBB configuration are shown. T wave inversion is noted at precordial leads. B. On follow-up, ECG evolution was noted. It shows deep T wave inversions in V1 to V3. ECG; electrocardiogram 40 Journal of Cardiac Arrhythmia
Figure 2. Documented monomorphic ventricular tachycardia with left bundle branch block configuration on 24 hours Holter recordings. A B Figure 3. Cardiac MRI showed bulging of RV apex with dyskinetic wall motion and focal aneurysm (bold white arrow) on systolic phase (A), and suspected linear enhancement (thin white arrow) along the RV myocardium, especially at apical portion (B). RV; right ventricles 41
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